Congenital Hypotrichosis

Congenital Hypotrichosis is a type of hair loss. It refers to a condition where no hair grows at all. It is not a type of alopecia, rather, in the case of Congenital Hypotrichosis, hair has not grown in the first place. Congenital Hypotrichoses start at birth. They are mostly due to genetics.


There are many types of Congenital Hypotrichoses. Those who have a type of Congenital Hypotrichosis, often have a mental illness. These conditions arevery rare. Those with conditions such as metaphyseal chondrodysplasia, Graham-Little syndrome, Ofuji syndrome, cartilage-hair hypoplasia, Jeanselme and Rime hypotrichosis, and Marie Unna hypotrichosis may experience Congenital Hypotrichosis too.

Some Congenital Hypotrichosis are important to mention such as Triangular Alopecia, Congenital Aplasia, and Congenital Atrichia. Let us look at them in detail:

Triangular Alopecia

Triangular Alopecia or Alopecia Triansgularis can affect an entirely healthy individual. Those with Triangular Alopecia have a triangular patch of skin above their temples.

Hair transplant to the bald patch is often very effective.

Congenital Aplasia

Congenital Aplasia or Aplasia Cutis Congenital is a condition where the skin does not fully form.

A baby with Congenital Aplasia may have an open ulcer/would like patch on their skin. If the patch is small, scabbing will occur, and it will result in a scar.

If the patch is big, an urgent surgery is required. Such a patch is potentially risky because it can cause infections and hemorrhage.

Congenital Atrichia

Congenital Atrichia is a condition that is caused by a single gene defect.

Individuals who have congenital atrichia, may have a full head when they are born. During their childhood, they lose all their hair, and it does not grow back. There is not enough information about the mechanism of Congenital Atrichia. It is mostly genetic but it can even develop in babies whose parents do not have Congenital Atrichia.

The diagnosis of Congenital Atrichia is sometimes mixed with Alopecia Universalis. Congenital Atricia is also very rare like the other Congenital Hypocthrises.


19 − eleven =